XH7GG7

ICD-11 MMS 2026-01

Primary myelofibrosis

Index terms

  • Primary myelofibrosis
  • Agnogenic myeloid metaplasia
  • Chronic idiopathic myelofibrosis
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  • Megakaryocytic myelosclerosis
  • Myelofibrosis as a result of myeloproliferative disease
  • Myelofibrosis with myeloid metaplasia
  • Myelosclerosis with myeloid metaplasia

Inclusions

  • Agnogenic myeloid metaplasia
  • Chronic idiopathic myelofibrosis
  • Megakaryocytic myelosclerosis
  • Myelofibrosis as a result of myeloproliferative disease
  • Myelofibrosis with myeloid metaplasia
  • Myelosclerosis with myeloid metaplasia

Sibling codes

  • XH0453 – Polycythaemia vera
  • XH07H5 – Myeloid and lymphoid neoplasms with PDGFRA rearrangement
  • XH1WR8 – Myeloid and lymphoid neoplasms with FGFR1 abnormalities
  • XH2WB4 – Myeloid or lymphoid neoplasm with PCM1-JAK2
  • XH4ZM5 – Essential thrombocythemia
  • XH51D2 – Chronic eosinophilic leukaemia
  • XH5HH7 – Myeloproliferative neoplasm, NOS
  • XH5NQ7 – Chronic neutrophilic leukaemia
  • XH6QD4 – Myeloid neoplasms with PDGFRB rearrangement

Foundation entity

Primary myelofibrosis – http://id.who.int/icd/entity/1407285327

Part of: X: Extension Codes