Catalog

Keratoglobus

No MMS code

Link to WHO Definition

Keratoglobus – http://id.who.int/icd/entity/1085899634

Keratoglobus shows globular protrusion of the cornea and diffuse corneal thinning most severe peripherally. There exists the congenital and the acquired form. The etiology is unknown. However, associations between keratoglobus and disorders such as Ehlers-Danlos type VI, Marfan syndrome, and the blue sclera syndrome indicate that the etiology may result from defects in collagen synthesis. There is also an association to vernal keratoconjunctivitis, dysthyroid ophthalmopathy, and chronic marginal blepharitis.