Catalog

Pyogenic arthritis - pyoderma gangrenosum - acne

No MMS code

Link to WHO Definition

Pyogenic arthritis - pyoderma gangrenosum - acne – http://id.who.int/icd/entity/1113124609

Pyogenic sterile arthritis, pyoderma gangrenosum, and acne (PAPA) syndrome is a rare pleiotropic autoinflammatory disorder of childhood, primarily affecting the joints and skin, characterised by pauciarticular, nonaxial, sometimes recurrent, sterile arthritis beginning in childhood; pyoderma gangrenosum; and severe cystic acne in adolescence and beyond.