Catalog

Congenital pulmonary trunk hypoplasia

No MMS code

Link to WHO Definition

Congenital pulmonary trunk hypoplasia – http://id.who.int/icd/entity/1152699781

A congenital cardiovascular malformation of the pulmonary trunk in which there is incomplete development or underdevelopment resulting in diffuse luminal narrowing (below the lower limit of normal adjusted for body size). The stenosis or hypoplasia may be isolated or associated with other cardiovascular lesions. Since the narrowing is distal to the pulmonary valve, it may also be known as supravalvar pulmonary stenosis.