Catalog

Hereditary mucoepithelial dysplasia

No MMS code

Link to WHO Definition

Hereditary mucoepithelial dysplasia – http://id.who.int/icd/entity/1167609602

This is a rare autosomal dominant multiepithelial disorder causing systemic maldevelopment of the epithelia and mucus membranes that line the surface of tissues and structures throughout the body, particularly affecting systems affiliated with mucosa, which includes the respiratory, digestive, urinary, reproductive and immune systems.