Catalog

Sporadic infantile bilateral striatal necrosis

No MMS code

Link to WHO Definition

Sporadic infantile bilateral striatal necrosis – http://id.who.int/icd/entity/1174703901

Sporadic infantile bilateral necrosis is the sporadic form of infantile bilateral striatal necrosis (IBSN), a syndrome of bilateral symmetric spongy degeneration of the caudate nucleus, putamen and globus pallidus characterised by developmental regression, choreoathetosis and dystonia progressing to spastic quadriparesis.