Catalog
Autoimmune generalised polymyoclonus
No MMS code
Link to WHO Definition
Autoimmune generalised polymyoclonus – http://id.who.int/icd/entity/1177707828
generalised body myoclonus has been described to occur in isolation as an autoimmune phenomenon and may be mistaken for generalised tremor. Accompanying neural autoantibodies may be found (e.g. voltage gated potassium complex autoantibodies) but other causes of myoclonus need to be excluded (e.g. drug induced). Associated autoantibodies: DPPX (dipeptidyl-peptidase–like protein-6); VGKC (LGI1, CASPR2) (voltage gated potassium channel complex antibodies ).