Catalog

Lobar holoprosencephaly

No MMS code

Link to WHO Definition

Lobar holoprosencephaly – http://id.who.int/icd/entity/121649206

Lobar holoprosencephaly is the mildest classical form of holoprosencephaly (HPE) characterised by separation of the right and left cerebral hemispheres and lateral ventricles with some continuity across the frontal neocortex, especially rostrally and ventrally. About 19% of HPE patients have lobar type.