Catalog
Defects in the complement system
Link to WHO Definition
Defects in the complement system – http://id.who.int/icd/entity/1222145690
Parents
Children
- Angioedema due to disordered complement activation or kinin metabolism
- Immunodeficiency with decay accelerating factor deficiency
- Immunodeficiency with factor I anomaly
- 4A00.13 Immunodeficiency with factor D anomaly
- Immunodeficiency with ficolin-3 deficiency
- Immunodeficiency with CD46 deficiency
- Immunodeficiency with MBL - [mannan-binding lectin] deficiency
- 4A00.12 Immunodeficiency with factor B deficiency
- Complement component C4b-binding protein deficiency
- 4A00.10 Immunodeficiency with an early component of complement deficiency
- Recurrent Neisseria infections due to factor D deficiency
- 4A00.11 Immunodeficiency with a late component of complement deficiency
- Immunodeficiency with MASP-2 deficiency
- Complement component C3 deficiency
- Immunodeficiency with CD59 deficiency
- Immunodeficiency with properdin deficiency
- Immunodeficiency with factor H anomaly