Catalog

Hypoplasminogenaemia

DA0D.3

Link to WHO Definition

Hypoplasminogenaemia – http://id.who.int/icd/entity/1240776230

Severe hypoplasminogenaemia or type 1 plasminogen (plg) deficiency is a systemic disease characterised by markedly impaired extracellular fibrinolysis leading to the formation of ligneous (fibrin-rich) pseudomembranes on mucosae during wound healing.

Parents