Catalog

Progressive familial intrahepatic cholestasis type 3

No MMS code

Link to WHO Definition

Progressive familial intrahepatic cholestasis type 3 – http://id.who.int/icd/entity/1276600959

Progressive familial intrahepatic cholestasis type 3 (PFIC3), a type of progressive familial intrahepatic cholestasis (PFIC), is a late-onset hereditary disorder in bile formation that is hepatocellular in origin characterised by cholestasis and evolving into secondary biliary cirrhosis.