Catalog
Pauci-immune proliferative glomerulonephritis
Link to WHO Definition
Pauci-immune proliferative glomerulonephritis – http://id.who.int/icd/entity/1359757645
A focal and segmental necrotising glomerulonephritis with no immune deposits (“pauci-immune”). Typical of glomerular involvement in anti-neutrophil cytoplasmic antibody (ANCA) mediated vasculitis – microscopic polyangiitis and Wegener's granulomatosis. Most but not all patients have circulation ANCA when there is active disease.