Catalog
Extrapontine central pontine myelinolysis
No MMS code
Link to WHO Definition
Extrapontine central pontine myelinolysis – http://id.who.int/icd/entity/1368206692
Extrapontine myelinolysis is often symmetrical and characterised by demyelinating lesions in the cerebral cortex, external capsule, basal ganglia, or midbrain with pontine and pallidal sparing. Extrapontine central pontine myelinolysis has a greater clinical heterogeneity with extrapontine involvement such as oromandibular and focal dystonia, spasmodic dysphonia, ataxia, parkinsonism, tremors, myoclonus, delirium and emotional lability due to involvement of basal ganglia.