Catalog
Pityriasis rubra pilaris type IV, circumscribed juvenile
No MMS code
Link to WHO Definition
Pityriasis rubra pilaris type IV, circumscribed juvenile – http://id.who.int/icd/entity/1377628152
This form of pityriasis rubra pilaris presents in prepubertal children with well circumscribed plaques of erythema and follicular hyperkeratosis on the elbows and knees. Palmoplantar keratoderma may be associated. It may remit during adolescence.