Catalog

Pulmonary interstitial glycogenosis

No MMS code

Link to WHO Definition

Pulmonary interstitial glycogenosis – http://id.who.int/icd/entity/1386580655

Pulmonary interstitial glycogenosis (PIG) is a rare non-lethal paediatric form of interstitial lung disease (ILD). Neonates present with respiratory distress syndrome shortly after birth. The characteristic histological feature of PIG is the accumulation of monoparticulate glycogen in interstitial cells on lung biopsy.