Catalog

Haemodialysis-associated pseudoporphyria

No MMS code

Link to WHO Definition

Haemodialysis-associated pseudoporphyria – http://id.who.int/icd/entity/1413317229

Pseudoporphyria is a photodistributed vesiculobullous disorder that clinically and histologically resembles porphyria cutanea tarda but without the associated porphyrin abnormalities. Its association with long-term haemodialysis is well recognised with estimates of its frequency as high as 18% reported in the past. The precise pathomechansim is poorly understood.