Catalog

Autosomal recessive polycystic kidney disease

No MMS code

Link to WHO Definition

Autosomal recessive polycystic kidney disease – http://id.who.int/icd/entity/1424110943

Autosomal recessive polycystic kidney disease (ARPKD) is an inherited condition characterised by multiple cysts affecting the collecting ducts giving rise to nephromegaly, arterial hypertension, urinary tract infection and chronic kidney disease (failure). Liver involvement (biliary abnormalities, cholangitis, portal hypertension) are frequently associated.