Catalog
Adult neuronal ceroid lipofuscinosis
No MMS code
Link to WHO Definition
Adult neuronal ceroid lipofuscinosis – http://id.who.int/icd/entity/1460031344
Adult neuronal ceroid lipofuscinoses (ANCLs) are a genetically heterogeneous group of neuronal ceroid lipofuscinoses (NCLs; see this term) with onset during the third decade of life, characterised by dementia, seizures and loss of motor capacities, and sometimes associated with visual loss caused by retinal degeneration.