Catalog

Adult neuronal ceroid lipofuscinosis

No MMS code

Link to WHO Definition

Adult neuronal ceroid lipofuscinosis – http://id.who.int/icd/entity/1460031344

Adult neuronal ceroid lipofuscinoses (ANCLs) are a genetically heterogeneous group of neuronal ceroid lipofuscinoses (NCLs; see this term) with onset during the third decade of life, characterised by dementia, seizures and loss of motor capacities, and sometimes associated with visual loss caused by retinal degeneration.

Parents