Catalog

Dilated cardiomyopathy due to mitochondrial myopathy

No MMS code

Link to WHO Definition

Dilated cardiomyopathy due to mitochondrial myopathy – http://id.who.int/icd/entity/1483420150

Dilated cardiomyopathy due to mitochondrial myopathy is a dilated cardiomyopathy in association with the presence of a mitochondrial abnormality that is known to be causally or likely causally associated with dilated cardiomyopathy. Patients may present with disease primarily involving the myocardium or be associated with more widespread myopathy and-or other organ manifestations. On biopsy, muscle tissue is usually characterised by 'ragged red' muscle fibres containing accumulations of glycogen and neutral lipids.