Catalog

Multiple mononeuropathy vasculitis with perinuclear antineutrophil cytoplasmic antibody-associated vasculitis

No MMS code

Link to WHO Definition

Multiple mononeuropathy vasculitis with perinuclear antineutrophil cytoplasmic antibody-associated vasculitis – http://id.who.int/icd/entity/1486202648

The perinuclear antineutrophilic cytoplasmic antibody (p-ANCA) is closely associated with rapidly progressing glomerulonephritis, microscopic polyangiitis, and allergic granulomatous angiitis. Mononeuropathy due to vasculitis is a neurological manifestation of these conditions. Associated neural autoantibodies include: pANCA (perinuclear anti-neutrophil Cytoplasmic Antibodies), neutrophilic cytoplasmic antigens, MPO-ANCA (Churg-Strauss), cANCA (Cytoplasmic anti-neutrophil Cytoplasmic Antibodies), Anti SSA/Ro (Soluble Substance A-Antigen, Robert-Antigen) and Centromere Fibrillarin (CREST).