Catalog

Intermediate-sized congenital melanocytic naevus

No MMS code

Link to WHO Definition

Intermediate-sized congenital melanocytic naevus – http://id.who.int/icd/entity/1530481185

A congenital melanocytic naevus (CMN) with a predicted or final adult maximal diameter of between 15 and 399 mm. The category of intermediate-sized CNM incorporates both medium (15-199 mm) and large 200-399 mm CMNs. They may be associated with multiple smaller satellite naevi (congenital or tardive), hypertrichosis, lipomas or benign proliferative nodules and they carry an increased risk of pre-pubertal cutaneous or central nervous system (CNS) melanoma. Leptomeningeal melanocytosis or focal neuromelanosis, found in 10-15% of cases, is infrequently associated with other CNS tumours, hydrocephalus, epilepsy, arachnoid cysts, or Dandy-Walker malformation.