Catalog

Pseudoxanthomatous nodular cutaneous mastocytosis

No MMS code

Link to WHO Definition

Pseudoxanthomatous nodular cutaneous mastocytosis – http://id.who.int/icd/entity/1549543493

Pseudoxanthomatous nodular cutaneous mastocytosis is a rare variant of cutaneous mastocytosis which presents in infancy with yellowish to red-brown papules and nodules which resemble xanthomata. Histologically there is infiltration of mast cells deep into the lower dermis. It tends to persist longer than other childhood forms of cutaneous mastocytosis.