Catalog

Dermatofibrosarcoma protuberans

No MMS code

Link to WHO Definition

Dermatofibrosarcoma protuberans – http://id.who.int/icd/entity/1579898301

Dermatofibrosarcoma protuberans is a locally invasive tumour arising in the dermis and showing fibroblastic differentiation. It typically presents as a very slowly enlarging firm nodular dermal mass on the trunk or proximal limbs. In its early stages it may be mistaken both clinically and histologically for a benign fibrous histiocytoma. Local recurrence after resection is common.