Catalog

Autoinflammatory granulomatosis of childhood

No MMS code

Link to WHO Definition

Autoinflammatory granulomatosis of childhood – http://id.who.int/icd/entity/1609700846

Granulomatous arthritis of childhood designates a chronic inflammatory disease characterised by granulomatous polyarthritis, uveitis and rash with a typical onset before 5 years. It can present in a familial form, called Blau Syndrome (BS), and a sporadic from, known as early onset sarcoidosis.

Parents

Children