Catalog

Hepatic manifestations of atypical fibrosis

No MMS code

Link to WHO Definition

Hepatic manifestations of atypical fibrosis – http://id.who.int/icd/entity/167415484

This refers to hepatic manifestations, in an atypical autosomal recessive genetic disorder that affects most critically the lungs, and also the pancreas, liver, and intestine. It is characterised by abnormal transport of chloride and sodium across an epithelium, leading to thick, viscous secretions.