Catalog
Idiopathic copper-associated cirrhosis
Link to WHO Definition
Idiopathic copper-associated cirrhosis – http://id.who.int/icd/entity/1692504835
Idiopathic copper-associated cirrhosis is a rare copper-overload liver disease characterised by a rapidly progressive liver cirrhosis from the first few years of life leading to hepatic insufficiency and harbouring a specific pathological aspect: pericellular fibrosis, inflammatory infiltration, hepatocyte necrosis, absence of steatosis, poor regeneration and histochemical copper staining.