Catalog

Pyodermatitis–pyostomatitis vegetans

No MMS code

Link to WHO Definition

Pyodermatitis–pyostomatitis vegetans – http://id.who.int/icd/entity/172394120

This rare disorder, which may be confined to the oral mucosa (pyostomatitis vegetans) or may affect the skin as well (pyodermatitis vegetans) is strongly associated with inflammatory bowel disease, particularly ulcerative colitis. It has also been associated with lymphoproliferative disorders, acne conglobata, hidradenitis suppurativa and dissecting cellulitis, amongst other conditions. The oral lesions consist of multiple pustules, plaques and erosions, which may have a ‘snail‐track’ appearance. The skin lesions are crusted papules and vegetating plaques with surrounding pustules, mainly affecting the major flexures and the scalp.