Catalog

Aplasia cutis congenita - intestinal lymphangiectasia

No MMS code

Link to WHO Definition

Aplasia cutis congenita - intestinal lymphangiectasia – http://id.who.int/icd/entity/1746934910

Aplasia cutis congenita - intestinal lymphangiectasia refers to the association of aplasia cutis congenita, a rare skin defect usually localised to the vertex and intestinal lymphangiectasia, presenting with generalised oedema and hypoproteinemia and lymphopenia.