Catalog

Dilated cardiomyopathy due to mucopolysaccharidoses

No MMS code

Link to WHO Definition

Dilated cardiomyopathy due to mucopolysaccharidoses – http://id.who.int/icd/entity/1767830504

Dilated cardiomyopathy due to mucopolysaccharidoses is the presence of dilated cardiomyopathy in association with the lysosomal accumulation of glycosaminoglycans (mucopolysaccharides). There are at least 7 main subtypes, with numerous associated mutations, with dilated cardiomyopathy noted in Type I (Hurler syndrome) and Type VI (Maroteaux-Lamy syndrome).