Catalog

Pityriasis rubra pilaris type V, atypical juvenile

No MMS code

Link to WHO Definition

Pityriasis rubra pilaris type V, atypical juvenile – http://id.who.int/icd/entity/178883706

This chronic childhood form of pityriasis rubra pilaris is uncommon and probably genetically heterogeneous. It may be present at birth or start in early childhood with widespread erythema and hyperkeratosis. Follicular hyperkeratosis is a prominent feature and keratoderma is common. Scleroderma-like changes have been described in the hands and feet.