Catalog
Epilepsy due to Rasmussen encephalitis
No MMS code
Link to WHO Definition
Epilepsy due to Rasmussen encephalitis – http://id.who.int/icd/entity/182666470
Epilepsy due to a chronic progressive disorder of unknown etiology, onset in childhood, associated with hemispheric atrophy, severe intractable focal epilepsy, intellectual decline, and hemiparesis. Neuropathologic features show inflammatory changes. More localised, protracted, or slowly progressive forms and age-related variants have been described. Immune response involving B- and T-cell-mediated processes provide evidence for an immune attack on synaptic antigens leading to seizures and cell death.