Catalog
WAGR syndrome
No MMS code
Link to WHO Definition
WAGR syndrome – http://id.who.int/icd/entity/1858307812
WAGR is an acronym for Wilms tumour-Aniridia-Genitourinary anomalies-mental Retardation syndrome. Wilms tumour or nephroblastoma is the most frequent renal tumour in children, accounting for 6 to 8% of paediatric cancers. About 1% of these tumours are associated with aniridia.
Parents
- LD2F.1 Syndromes with multiple structural anomalies, not of environmental origin
- LD44.B1 Deletions of the short arm of chromosome 11
- Dysgenetic 46,XY disorder of sex development
- Inherited cancer-predisposing syndromes
- Syndromic conditions with disorders of intellectual development as a relevant clinical feature
- Nephroblastoma