Catalog

Von Willebrand disease type 1

No MMS code

Link to WHO Definition

Von Willebrand disease type 1 – http://id.who.int/icd/entity/1861858008

Type 1 von Willebrand disease (type 1 VWD) is a form of VWD (see this term) characterised by a bleeding disorder associated with a partial quantitative plasmatic deficiency of an otherwise structurally and functionally normal Willebrand factor (von Willebrand factor; VWF). The type 1 disease is considered to be the most common form of VWD, accounting for between 50 and 75% of cases but its prevalence is probably overestimated. Age of onset of bleeding anomalies varies, with earlier onset and more severe symptoms being associated with more severe VWF deficiency.