Catalog

Infantile myofibroma or myofibromatosis

No MMS code

Link to WHO Definition

Infantile myofibroma or myofibromatosis – http://id.who.int/icd/entity/18628852

Infantile myofibromatosis is an unusual mesenchymal disorder characterised by the proliferation of tumours in the skin, muscle, bone, and viscera. Although it is a rare condition, it is the most common fibrous tumour of infancy. There are two distinguishable types of infantile myofibromatosis: the solitary type, defined by the presence of one nodule in the skin, muscle, bone or subcutaneous tissue, and the multicentric type, which can be further divided into two sub-types. The first sub-type is associated with multicentric lesions but no visceral involvement, while in the second type, visceral involvement is present.