Catalog

Atypical teratoid rhabdoid tumour of brain

No MMS code

Link to WHO Definition

Atypical teratoid rhabdoid tumour of brain – http://id.who.int/icd/entity/1864152995

An aggressive malignant embryonal neoplasm arising from the central nervous system. It is composed of cells with a large eccentric nucleus, prominent nucleolus, and abundant cytoplasm. It may be associated with loss of chromosome 22. The vast majority of cases occur in childhood. Symptoms include lethargy, vomiting, cranial nerve palsy, headache, and hemiplegia.