Catalog

Hereditary factor VII deficiency

No MMS code

Link to WHO Definition

Hereditary factor VII deficiency – http://id.who.int/icd/entity/2034923927

Factor VII (FVII) deficiency is a rare hereditary haemorrhagic disease caused by the diminution or absence of this coagulation factor. The clinical expression of this disorder is highly variable, and no consistent relationship has been found between the severity of the haemorrhagic syndrome and the residual levels of FVII activity.