Catalog

Steatocystoma multiplex

No MMS code

Link to WHO Definition

Steatocystoma multiplex – http://id.who.int/icd/entity/2085770731

Steatocystoma multiplex is a rare autosomal dominant genodermatosis characterised by the development of multiple intradermal cysts with sebaceous gland lobules in their wall and sebum in their lumen. It usually first manifests in adolescence or early adult life with multiple smooth compressible dermal nodules involving the trunk, particularly the presternal area, and proximal limbs. Suppuration and scarring commonly occur.

Parents