Catalog

Juvenile dermatomyositis with lipodystrophy

No MMS code

Link to WHO Definition

Juvenile dermatomyositis with lipodystrophy – http://id.who.int/icd/entity/2133970870

Juvenile dermatomyositis with lipodystrophy is a chronic systemic autoimmune disease characterised by early-onset proximal weakness and characteristic skin rashes, associated with loss of subcutaneous fat in a localised or generalised distribution, frequently with resultant metabolic abnormalities such as insulin resistance, diabetes and hyperlipidaemia. These patients have a loss of mature, functional adipocytes, as opposed to an absence of lipid in otherwise normal adipocytes.