Catalog

Somatostatinoma

No MMS code

Link to WHO Definition

Somatostatinoma – http://id.who.int/icd/entity/219879696

A rare, usually malignant neuroendocrine tumour arizing from delta cells. This neoplasm produces large amounts of somatostatin, which may result in a syndrome characterised by diarrhea, steatorrhea, weight loss, and gastric hyposecretion. Sixty percent are found in the pancreas and 40% in the duodenum or jejunum. The peak incidence occurs between 40 and 60 years of age; women are affected more than men by 2:1.