Catalog

Congenital thrombotic thrombocytopenic purpura due to ADAMTS-13 deficiency

No MMS code

Link to WHO Definition

Congenital thrombotic thrombocytopenic purpura due to ADAMTS-13 deficiency – http://id.who.int/icd/entity/258428739

This is a rare disorder of the blood-coagulation system, causing extensive microscopic clots to form in the small blood vessels throughout the body, due to ADAMTS-13 deficiency.