Catalog

Dementia due to Gerstmann-Staussler-Sheinker syndrome

No MMS code

Link to WHO Definition

Dementia due to Gerstmann-Staussler-Sheinker syndrome – http://id.who.int/icd/entity/290481170

Dementia due to an autosomal dominant hereditary disease linked to a mutation in the prion protein gene. It can have a slowly progressive course. Clinical presentation typically includes gait imbalance, but can also include parkinsonism and other motor symptoms.