Catalog

Corticobasal degeneration

No MMS code

Link to WHO Definition

Corticobasal degeneration – http://id.who.int/icd/entity/348567584

Corticobasal degeneration is a neurodegenerative disorder of the elderly which affects subcortical, then cortical brain areas and presents with a slowly progressive, unilateral jerky, tremulous, akinetic, rigid and apraxic limb held in a fixed dystonic posture and displaying the alien limb syndrome. The behavioural manifestations may also include language disturbances and frontal-lobe-type behaviour. The pathology is pleomorphic and the progression is hard to predict clinically.