Catalog

Noninflammatory inclusion body myopathy

4A41.21

Link to WHO Definition

Noninflammatory inclusion body myopathy – http://id.who.int/icd/entity/404396176

Noninflammatory inclusion body myopathy (IBM) is an idiopathic muscle disorder without inflammatory exudates and expression of class I major histocompatibility complex. Rimmed vacuoles and “IBM-like” filaments without inflammatory cells are described in muscle biopsy.

Parents

Children