Catalog

Dementia due to fatal familial insomnia

No MMS code

Link to WHO Definition

Dementia due to fatal familial insomnia – http://id.who.int/icd/entity/467518334

Dementia due to an autosomal dominant hereditary disease linked to mutation in the prion protein gene. It has a rapidly progressive course. Concomitant symptoms include insomnia, autonomic dysregulation, and sometimes incoordination and movement disorder.