Catalog

Smouldering systemic mastocytosis

No MMS code

Link to WHO Definition

Smouldering systemic mastocytosis – http://id.who.int/icd/entity/481663898

Smouldering systemic mastocytosis is a type of systemic mastocytosis. This clonal haematological disease with a slow progression results in an accumulation of neoplastic mast cells in the visceral organs over time and patients that present with splenomegaly, hypercellular marrow and, in some cases, urticaria pigmentosum-like skin lesions.