Catalog

Juvenile dermatomyositis with necrotising cutaneous vasculitis

No MMS code

Link to WHO Definition

Juvenile dermatomyositis with necrotising cutaneous vasculitis – http://id.who.int/icd/entity/504741085

Type of idiopathic inflammatory myopathy that is characterized by rash accompanied by muscle weakness, anorexia, and fatigue. Juvenile form presents more insidiously with muscle weakness, particularly of the neck flexors, often preceded by fatigue and low grade fevers. Associated with heliotropic rash, periorbital erythema, Gottron papules over the knuckles, elbows, and knees, and periungal telangectasias. Juvenile form is associated with greater involvement of blood vessels and vasculopathy compared to adult form.