Catalog

Holoprosencephaly, middle interhemispheric variant

No MMS code

Link to WHO Definition

Holoprosencephaly, middle interhemispheric variant – http://id.who.int/icd/entity/520338638

Midline interhemispheric variant of holoprosencephaly or syntelencephaly is a form of holoprosencephaly (HPE) characterised by non-separation of the posterior frontal and parietal lobes, normally-formed callosal genu and splenium, absence of the callosal body, normally-separated hypothalamus and lentiform nuclei, and frequent heterotopic grey matter.