Catalog
Parkinsonism due to prion diseases
No MMS code
Link to WHO Definition
Parkinsonism due to prion diseases – http://id.who.int/icd/entity/537542868
Parkinsonism can be an atypical progressive feature of human prion diseases such as Creutzfeldt–Jakob disease or Gerstmann-Straussler-Scheinker Syndrome. Caused by point mutations in prion protein (PRNP) that cause dementia, myoclonus, and ataxia.