Catalog
Crouzon syndrome - acanthosis nigricans
No MMS code
Link to WHO Definition
Crouzon syndrome - acanthosis nigricans – http://id.who.int/icd/entity/549448576
Crouzon syndrome - acanthosis nigricans is the association of Crouzon syndrome, occurring in 5% of cases, with acanthosis nigricans. Chiari malformation, hydrocephalus, and atresia or stenosis of the choanas may suggest the diagnosis of Crouzon syndrome with AN even before acanthosis appears.