Catalog

Systemic mastocytosis with an associated clonal haematologic non-mast cell lineage disease

No MMS code

Link to WHO Definition

Systemic mastocytosis with an associated clonal haematologic non-mast cell lineage disease – http://id.who.int/icd/entity/572179318

Systemic mastocytosis with an associated clonal haematological non-mast cell lineage disease is a form of systemic mastocytosis associated with malignancy (other than mast cell leukaemia; see this term). It represents less than 10% of cases of systemic mastocytosis. This condition is usually indolent, but may rarely be aggressive.